características ecocardiográficas da cardiomiopatia não-compactada: diagnóstico perdido ou errôneo características ecocardiográficas de la miocardiopatía no compactada: diagnóstico perdido o erróneo echocardiographic features of non-compaction cardiomyopathy: missed and misdiagnosed disease

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2009
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Abstract
A cardiomiopatia não-compactada é uma doença rara, anatomicamente caracterizada por um padrão trabecular proeminente e recessos intra-trabeculares profundos. Suas manifestações clínicas incluem disfunção ventricular grave arritmias, embolismo sistêmico e morte súbita. Nesse estudo, dois casos de pacientes de idades diferentes com cardiomiopatia não-compactada são descritos: uma criança do sexo masculino em idade escolar, cuja patologia estava associada com estenose mitral e regurgitação e um paciente adulto do sexo feminino, com 50 anos de idade e histórico de hipertensão arterial e insuficiência cardíaca.
La miocardiopatía no compactada es una enfermedad rara, anatómicamente caracterizada por un patrón trabecular prominente y recesos intertrabeculares profundos. Sus manifestaciones clínicas incluyen disfunção ventricular gravem arritmias, embolismo sistémico y muerte súbita. En este estudio se describen dos casos de pacientes de edades diferentes con miocardiopatía no compactada: un niño de sexo masculino en edad escolar, cuya patología estaba asociada a estenosis mitral y regurgitación, y un paciente adulto del sexo femenino, con 50 años de edad e historia de hipertensión arterial e insuficiencia cardíaca.
Non-compaction cardiomyopathy is a rare disease, anatomically characterized by a prominent trabecular pattern and deep intertrabecular recesses. Its clinical manifestations include severe left ventricular dysfunction, arrhythmias, systemic embolism, and sudden death. In this report, two cases of patients of different ages with non-compaction cardiomyopathy are described: a male schoolboy whose pathology was associated with mitral stenosis and regurgitation and a 50-year-old female with history of high blood pressure and cardiac failure.
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Authors ;Francisco Martínez-Baca López;Rosa Marisol Alonso Bravo;Domingo Arturo Rodríguez Huerta
Journal revista cubana de ciencias informáticas
Year 2009
DOI
10.1590/S0066-782X2009000800024
URL
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