Van Praagh Type A3 Truncus Arteriosus in a 47-Year-Old man: Correcting a Misdiagnosis via Multimodal Imaging——A Case Report

Clicks: 12
ID: 332919
2026
Free PDF
Article Quality & Performance Metrics
Overall Quality
Not rated
Combines reader engagement with the AI quality analysis. This article has not been analysed, so there is no overall score — reader engagement is measured and shown alongside.
AI Quality Assessment
Not analyzed
Readership in this journal
Emerging

Ranked #316 of 408 articles by views in European Heart Journal - Case Reports

Most read Least read

Bar heights use a square-root scale. Only the 120 most-read articles are drawn; the journal has 408 in total.

Mint this article as an NFT
Not yet minted

Create a permanent, verifiable on-chain record of this article on the Scimatic Network. The NFT is held in your Journament account, and you can withdraw it to your own wallet at any time.

5 SUSD one-off · no wallet required
Sign in to mint
Abstract
Abstract Background Persistent truncus arteriosus (TA) is a rare conotruncal anomaly characterized by a single arterial trunk supplying the systemic, pulmonary, and coronary circulations. Unrepaired survival into the fifth decade is exceptional. This case highlights the complementary roles of transthoracic echocardiography (TTE) and computed tomography angiography (CTA) in resolving longstanding diagnostic uncertainty and delineating complex pulmonary arterial and collateral anatomy. Case summary A 47-year-old man diagnosed with tetralogy of Fallot after birth, but who received no corrective treatment or subsequent cardiac follow-up, presented with recurrent haemoptysis. He had marked cyanosis, severe hypoxaemia (SpO2 84%), and secondary erythrocytosis, but no overt decompensated heart failure. TTE demonstrated a common trunk overriding of a large ventricular septal defect with bidirectional shunting, moderate truncal valve regurgitation, and preserved biventricular systolic function, but failed to clearly define the origin of the left pulmonary artery. CTA established Van Praagh type A3 TA, with the left pulmonary artery arising from the distal common trunk, absence of the native right pulmonary artery, and collateral-dependent right lung perfusion. Cardiac catheterisation was declined. Haemoptysis subsided with conservative treatment, but severe hypoxaemia persisted (SpO2 84%), and the patient requested early discharge against medical advice. Conclusion Multimodal imaging corrected a longstanding diagnostic misclassification, clarified the asymmetric pulmonary arterial and collateral anatomy, and suggested possible mechanisms for prolonged survival and haemoptysis. Although reclassification did not alter the immediate conservative management, it refined the differential diagnosis and provided an anatomical basis for future surveillance.
Reference Key
openalex_W7222950395 Use this key to autocite in the manuscript while using SciMatic Manuscript Manager or Thesis Manager
Authors Ge Zhengdan, 姚豪华, Yongshi Wang, Yang Xue, Cuizhen Pan
Are you one of these authors? Claim your profile
Journal European Heart Journal - Case Reports
Year 2026
DOI
10.1093/ehjcr/ytag769
URL
https://doi.org/10.1093/ehjcr/ytag769
Keywords Keywords not found

Citations

No citations found. To add a citation, contact the admin at info@scimatic.org

Comments

No comments yet. Be the first to comment on this article.